Vol. 2, Issue 1, Part A (2020)

Aortopulmonary window a rare congenital abnormality of the great vessels, manifests as heart failure in the early age with less chances of survival beyond first decade. It presenting as the Eisenmenger syndrome is rare. A 16 year female with breathlessness and bluish discoloration of 3 months duration on evaluation found to have a large aortopulmonary window with reversal of shunt on echocardiography. She was kept on pulmonary vasodilators and oral anticoagulants. she improved symptomatically as assessed by improved six minute walk test distance.